Giant Fibroma in Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome Patient: A Case Report

Abstract

MRKH syndrome is a rare form of genital malformation (the incidence is for 1/4000-5000 people). The MRKH patient shows no sign of uterus although its two annexes develop normally. People with MRKH do not have periods although their secondary sexual signs are normal. The fact that the fibrous cells in the Müller's fibrous strand grow into uterine fibroid tumors is very rare but often causes difficulties in diagnosing the origin of the tumor. Surgical removal of the tumor to prevent other tumors from developing is the most effective treatment.

 Keywords

Mayer-Rokitansky-Kuster-Hauser, fibroma.

References

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